Overview
Double-outlet right ventricle (DORV) is a congenital heart defect where both the body’s main artery (aorta) and the lung artery (pulmonary artery) connect to the right ventricle instead of their usual positions. Typically, the aorta connects to the left ventricle, and the pulmonary artery connects to the right ventricle.
Types of Double-outlet right ventricle (DORV)
- ubpulmonary (Taussig-Bing) Type: The pulmonary artery arises from the right ventricle and overrides the ventricular septal defect (VSD).
- Subaortic (Eisenmenger) Type: The aorta arises from the right ventricle and overrides the VSD.
Causes of Double-outlet right ventricle (DORV)
The exact cause of DORV is not always clear, but it occurs during fetal development. Genetic factors and environmental influences may play a role.
Risk Factors of Double-outlet right ventricle (DORV)
- Maternal Factors: Poorly controlled diabetes during pregnancy or exposure to certain medications or infections.
- Genetic Factors: Family history of congenital heart defects.
- Environmental Factors: Exposure to toxins or radiation during pregnancy.
Symptoms of Double-outlet right ventricle (DORV)
1. Cyanosis (bluish skin due to low oxygen levels)
2. Rapid breathing.
3. Fatigue.
4. Poor feeding and growth.
Preventions of Double-outlet right ventricle (DORV)
Preventing DORV is challenging, but maintaining a healthy lifestyle during pregnancy and avoiding harmful substances can reduce the risk.
Diagnosis of Double-outlet right ventricle (DORV)
- Echocardiogram: Sound waves create images of the heart, showing blood flow and heart valve function.
- Additional tests may include cardiac CT scans, MRI scans, and cardiac catheterization.
Treatment for Double-outlet right ventricle (DORV)
- Surgery: Repairing the defect is essential. Surgical options include:
- Creating a tunnel between the left ventricle and the aorta.
- Correcting the positions of the aorta and pulmonary artery.
- Patching the VSD.
- Connecting the right ventricle to the pulmonary artery.
- Lifelong Follow-Up: Regular check-ups and monitoring are crucial.
When to seek medical attention ?
If your child shows symptoms like cyanosis, rapid breathing, or poor feeding, seek medical attention promptly.
